Patient | Time | Age | MRI | Ttt | SLEDAI | Neurological features | Mood score | Dep score | Anx score | Rhyt score | vHal score | aHal score | Cat score | Cog score | Slow score | Conf score | Global NP score |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
#1 | Dg PET1 | 16y9m 18y3m | Sc,Inf | GLpo/MMF | 13 8 | - - | 2 0 | 3 0 | 2 2 | 0 0 | 0 0 | 0 0 | 0 0 | 2 0 | 2 0 | 0 0 | 11 2 |
#2 | Dg PET1 | 14y 14y7m | Sc | Gpo/MMF/H | 42 0 | - - | 0 1 | 0 0 | 0 0 | 2 1 | 2 0 | 2 0 | 0 0 | 2 1 | 2 0 | 0 0 | 10 3 |
#3 | Dg PET1 | 11y7m 11y8m | Nl | Gpo/CYC/H | 26 0 | - - | 0 0 | 0 0 | 0 0 | 2 0 | 0 0 | 2 0 | 0 0 | 3 0 | 0 0 | 0 0 | 7 0 |
#4 | Dg PET1 | 15y3m 15y11m | Sc | Gpo/MMF/H | 24 18 | - - | 1 1 | 1 1 | 0 0 | 1 0 | 2 0 | 1 0 | 0 0 | 1 1 | 0 0 | 0 0 | 7 3 |
#5 | Dg PET1 PET2 | 15y4m 15y6m 16y | Sc Sc | Gpo/CYC Gpo | 36 36 NA | Pyr SD, Tetraplegia Distal motor deficit - | 0 0 0 | 0 0 0 | 0 0 0 | 3 0 0 | 2 0 0 | 1 0 0 | 0 0 0 | 3 1 0 | 2 0 0 | 0 0 0 | 11 1 0 |
#6 | Dg PET1 PET2 | 16y4m 16y4m 17y9m | Nl Nl | Gpo/H Gpo/MMF/H | 8 8 8 | - - - | 3 3 2 | 3 3 2 | 2 2 3 | 0 0 2 | 2 2 0 | 2 2 0 | 0 0 0 | 1 1 0 | 2 2 0 | 0 0 0 | 15 15 9 |
#7 | Dg (CT)PET1 PET2 | 15y4m 16y1m 16y10m | Nl Nl | Gpo/MMF/H MMF/H | 21 NA 20 | - - - | 2 0 2 | 2 0 2 | 0 0 0 | 2 1 2 | 1 0 2 | 0 0 2 | 0 0 0 | 2 0 0 | 1 0 2 | 0 0 0 | 10 1 12 |
#8 | Dg PET1 PET2 | 14y 15y5m 16y2m | Nl Nl | MMF/H - | NA NA NA | - - - | 0 0 | 0 1 | 0 1 | 0 0 | 0 0 | 0 0 | 0 0 | 0 1 | 0 0 | 0 0 | 0 3 |
#9 | Dg PET1 PET2 | 11y3m 11y5m 12y4m | At At | Gpo/END Gpo/MMF | 48 6 6 | Pyr SD - - | 1 0 0 | 0 0 0 | 0 0 0 | 0 1 0 | 3 0 0 | 3 0 0 | 3 1 0 | 3 2 1 | 3 0 0 | 3 0 0 | 19 4 1 |
#10 | Dg (CT)PET1 (CT)PET2 | 14y11m 15y1m 15y7m | At | Gpo/CYC/H Gpo/H | 23 10 16 | Pyr SD - - | 0 2 1 | 0 1 1 | 0 1 3 | 1 2 0 | 0 0 0 | 0 0 0 | 0 0 0 | 1 0 1 | 0 0 2 | 0 0 0 | 2 6 8 |
#11 | Dg PET1 PET2 PET3 | 13y5m 14y7m 14y10m 16y5m | Nl Nl Nl | Gpo/ABA/H Gpo/ABA/H Gpo/ABA/H | 22 2 2 22 | - - - - | 3 1 1 2 | 3 1 1 3 | 0 0 0 0 | 0 0 0 3 | 2 1 0 0 | 2 1 0 0 | 0 0 0 0 | 1 0 1 2 | 0 0 0 0 | 0 0 0 0 | 11 4 3 10 |