From: 18F-florbetaben whole-body PET/MRI for evaluation of systemic amyloid deposition
Characteristics | Patients | ||||||||
---|---|---|---|---|---|---|---|---|---|
1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 | 9 | |
Age | 61 | 66 | 70 | 80 | 72 | 86 | 62 | 66 | 62 |
Sex | F | M | M | M | M | M | M | M | M |
Diagnosis | AL Lambda | AL Lambda | AL Kappa | HCM | AL Lambda | HCM | AL Lambda | AL Lambda | AL Lambda |
Biopsy | Abdominal Fata | Tongue Lungs BMb | Kidneys | – | Myocardial BMa | – | Abdominal fat BMb | GI BMb | Kidneys |
Organs involvementa | Heart Kidney Larynx/GI | Heart Kidneys | – | – | – | – | Heart | Kidneys | Heart |
Troponin I (< 0.1 ng/ml) | < 0.1 | < 0.1 | < 0.1 | < 0.1 | 1.986 | < 0.1 | < 0.01 | < 0.1 | 0.08 |
NT-proBNP (< 300 mg/ml) | 2.086 | 8.804 | 631 | 3.188 | 1.804 | N/A | 330 | 183 | 575 |
Creatinine (0.50–1.2 mg/dl) | 0.49 | 1.6 | 1.76 | 1.45 | 1.66 | 1.03 | 0.7 | 1.8 | 2.61 |
Alb/creat ratio (< 30 mg/g) | 2.214 | 1.972 | 54 | N/A | N/A | N/A | N/A | N/A | N/A |
Free Lambda light chain (0.6–2.6 mg/dl) | 3.1 | 16.7 | 1 | N/A | 0.3 | N/A | 2.7 | 4.3 | 8.4 |
Free Kappa light chain (0.3–2.0 mg/dl) | 1.5 | 1.5 | 1.7 | N/A | 0.1 | N/A | 0.4 | 3.5 | 9.2 |
Free K/L ratio (0.3–1.6) | 0.4 | 0.1 | 1.7 | N/A | 0.3 | N/A | 0.1 | 0.8 | 1.1 |